Desmoplastic small round-cell tumour of the peritoneal cavity: case report and literature review
Authors
Tsoukalas, NKiakou, M
Nakos, G
Tolia, M
Galanopoulos, M
Tsapakidis, K
Kamposioras, Konstantinos
Christofyllakis, C
Dimitrakopoulos, G
Sambaziotis, D
Affiliation
Department of Oncology, Veterans Hospital (NIMTS), Athens, GreeceIssue Date
2020
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Desmoplastic small round-cell tumour is a very rare neoplasm, which usually arises from the abdominal or pelvic peritoneum of adolescents and young adults. Early diagnosis is difficult, because most tumours present with non-specific gastrointestinal symptoms after a long asymptomatic period. It is generally a very aggressive tumour, which grows rapidly with poor prognosis and an overall five-year survival rate of 15% despite multimodal treatment. Despite multiple treatment strategies, the management of desmoplastic small round-cell tumour still remains a clinical challenge and no consensus about a therapeutic protocol has been established. A 35-year-old man presented with mild abdominal pain, constipation and weight gain, and was eventually diagnosed with desmoplastic small round-cell tumour, which was shown to be limited to the abdomen. After incomplete debulking surgery, radiotherapy and chemotherapy, he developed multiple metastatic nodular foci in chest and the pleura and, unfortunately, he died due to disease progression.Citation
Tsoukalas N, Kiakou M, Nakos G, Tolia M, Galanopoulos M, Tsapakidis K, et al. Desmoplastic small round-cell tumour of the peritoneal cavity: case report and literature review. Ann R Coll Surg Engl. 2020:1-5.Journal
Annals of the Royal College of Surgeons of EnglandDOI
10.1308/rcsann.2019.0180PubMed ID
31973562Additional Links
https://dx.doi.org/10.1308/rcsann.2019.0180Type
ArticleLanguage
enae974a485f413a2113503eed53cd6c53
10.1308/rcsann.2019.0180
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