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dc.contributor.authorWilks, D J
dc.contributor.authorMowatt, David J
dc.contributor.authorMerchant, W
dc.contributor.authorLiddington, M I
dc.date.accessioned2012-11-09T17:20:20Z
dc.date.available2012-11-09T17:20:20Z
dc.date.issued2012-05
dc.identifier.citationFacial paediatric desmoid fibromatosis: a case series, literature review and management algorithm. 2012, 65 (5):564-71 J Plast Reconstr Aesthet Surgen_GB
dc.identifier.issn1878-0539
dc.identifier.pmid22154716
dc.identifier.doi10.1016/j.bjps.2011.09.027
dc.identifier.urihttp://hdl.handle.net/10541/251636
dc.description.abstractDesmoid fibromatosis (also known as infantile or aggressive fibromatosis) is a rare soft tissue tumour that is occasionally seen in children. Although histologically benign, its growth pattern is highly aggressive often showing invasion of surrounding musculature and bone. Frequently found in cosmetically sensitive areas, complete excision can present a challenging problem. However, incomplete surgical excision is associated with high recurrence rates and although the disease responds to chemo and radiotherapy, both carry significant risks in young children. The management of four paediatric desmoid fibromatoses occurring in the midface is discussed. The recent and pertinent literature is comprehensively reviewed and an algorithm for the management of paediatric desmoid fibromatoses is proposed.
dc.language.isoenen
dc.rightsArchived with thanks to Journal of plastic, reconstructive & aesthetic surgery : JPRASen_GB
dc.subject.meshAlgorithms
dc.subject.meshBiopsy
dc.subject.meshChild, Preschool
dc.subject.meshFacial Neoplasms
dc.subject.meshFemale
dc.subject.meshFibromatosis, Aggressive
dc.subject.meshHumans
dc.subject.meshInfant
dc.subject.meshMale
dc.subject.meshNeoplasm Recurrence, Local
dc.subject.meshPrognosis
dc.titleFacial paediatric desmoid fibromatosis: a case series, literature review and management algorithm.en
dc.typeArticleen
dc.contributor.departmentDepartment of Plastic and Reconstructive Surgery, Leeds Teaching Hospitals NHS Trust, Leeds, UK.en_GB
dc.identifier.journalJournal of Plastic, Reconstructive & Aesthetic Surgeryen_GB
html.description.abstractDesmoid fibromatosis (also known as infantile or aggressive fibromatosis) is a rare soft tissue tumour that is occasionally seen in children. Although histologically benign, its growth pattern is highly aggressive often showing invasion of surrounding musculature and bone. Frequently found in cosmetically sensitive areas, complete excision can present a challenging problem. However, incomplete surgical excision is associated with high recurrence rates and although the disease responds to chemo and radiotherapy, both carry significant risks in young children. The management of four paediatric desmoid fibromatoses occurring in the midface is discussed. The recent and pertinent literature is comprehensively reviewed and an algorithm for the management of paediatric desmoid fibromatoses is proposed.


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