Affiliation
Department of Hepatopancreatobiliary and General Surgery, North Manchester General Hospital, Manchester, UK.Issue Date
2012-06
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Show full item recordAbstract
A 48-year-old woman presented with chest symptoms. Multiple lesions seen on chest imaging were found to be pulmonary chondromas following surgical resection. Whole body magnetic resonance scan performed to investigate the possibility of Carney triad demonstrated a gastric lesion. This was resected and found to be a gastrointestinal stromal tumor. No evidence of paragangliomata was found on imaging. A diagnosis of incomplete Carney triad was made. Carney triad is a rare multiple neoplastic association of pulmonary chondroma, gastrointestinal stromal tumor, and paraganglioma. At least 2 tumors are required for diagnosis. Most patients are young women. No genetic cause has been identified. Management involves surgical resection of tumors and follow-up for recurrence and investigation for other elements of the triad.Citation
Two out of three required: a case of incomplete Carney triad. 2012, 20 (3):265-8 Int J Surg PatholJournal
International Journal of Surgical PathologyDOI
10.1177/1066896911415668PubMed ID
21791484Type
ArticleLanguage
enISSN
1940-2465ae974a485f413a2113503eed53cd6c53
10.1177/1066896911415668
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