Soft-tissue extrarenal rhabdoid tumor with a unique long-term survival.

2.50
Hdl Handle:
http://hdl.handle.net/10541/84406
Title:
Soft-tissue extrarenal rhabdoid tumor with a unique long-term survival.
Authors:
Fabre, A; Eyden, Brian P; Ali, H H
Abstract:
Rhabdoid tumors of kidney and extrarenal rhabdoid tumors are identified by a round-epithelioid cell morphology and a bland immunophenotype, but a distinctive ultrastructure dominated by paranuclear whorls of intermediate filaments, most usually of vimentin. These tumors are also known to be highly aggressive malignancies, which, typically, bear a poor prognosis, frequently measured in months following initial presentation. The authors record the case a soft-tissue rhabdoid tumor in a 12-year-old boy with a unique long-term survival in excess of 16 years. The features of this case are documented, with a brief summary of histological, immunohistochemical, ultrastructural, and genetic characteristics of this entity.
Affiliation:
Histopathology Department, St Mary's Hospital, London, UK.
Citation:
Soft-tissue extrarenal rhabdoid tumor with a unique long-term survival. 2004, 28 (1):49-52 Ultrastruct Pathol
Journal:
Ultrastructural Pathology
Issue Date:
2004
URI:
http://hdl.handle.net/10541/84406
PubMed ID:
14967599
Type:
Article
Language:
en
ISSN:
0191-3123
Appears in Collections:
All Christie Publications

Full metadata record

DC FieldValue Language
dc.contributor.authorFabre, Aen
dc.contributor.authorEyden, Brian Pen
dc.contributor.authorAli, H Hen
dc.date.accessioned2009-10-19T15:32:48Z-
dc.date.available2009-10-19T15:32:48Z-
dc.date.issued2004-
dc.identifier.citationSoft-tissue extrarenal rhabdoid tumor with a unique long-term survival. 2004, 28 (1):49-52 Ultrastruct Patholen
dc.identifier.issn0191-3123-
dc.identifier.pmid14967599-
dc.identifier.urihttp://hdl.handle.net/10541/84406-
dc.description.abstractRhabdoid tumors of kidney and extrarenal rhabdoid tumors are identified by a round-epithelioid cell morphology and a bland immunophenotype, but a distinctive ultrastructure dominated by paranuclear whorls of intermediate filaments, most usually of vimentin. These tumors are also known to be highly aggressive malignancies, which, typically, bear a poor prognosis, frequently measured in months following initial presentation. The authors record the case a soft-tissue rhabdoid tumor in a 12-year-old boy with a unique long-term survival in excess of 16 years. The features of this case are documented, with a brief summary of histological, immunohistochemical, ultrastructural, and genetic characteristics of this entity.en
dc.language.isoenen
dc.subjectRhabdoid Tumoursen
dc.subjectSoft Tissue Canceren
dc.subjectBiological Tumour Markersen
dc.subject.meshAntineoplastic Combined Chemotherapy Protocols-
dc.subject.meshChemotherapy, Adjuvant-
dc.subject.meshChild-
dc.subject.meshDisease-Free Survival-
dc.subject.meshHumans-
dc.subject.meshImmunoenzyme Techniques-
dc.subject.meshIntermediate Filaments-
dc.subject.meshMale-
dc.subject.meshMicroscopy, Electron-
dc.subject.meshRhabdoid Tumor-
dc.subject.meshSoft Tissue Neoplasms-
dc.subject.meshTumor Markers, Biological-
dc.titleSoft-tissue extrarenal rhabdoid tumor with a unique long-term survival.en
dc.typeArticleen
dc.contributor.departmentHistopathology Department, St Mary's Hospital, London, UK.en
dc.identifier.journalUltrastructural Pathologyen

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